A case of achondroplasia for emergency cesarean section

Authors

  • Asha Pun Pokhara Academy of Health Sciences, Ramghat-10, Pokhara 33700
  • Rohini Sigdel Pokhara Academy of Health Sciences, Ramghat-10, Pokhara 33700

Keywords:

Cesarean delivery, Dwarf, Short stature, Spinal anesthesia

Abstract

Patients with achondroplasia present with various anatomical and physiological features including skeletal, neurological, and cardiopulmonary abnormalities. These characteristics create a difficult scenario wherein the selection of general or regional anesthesia becomes a dilemma. Moreover, pregnancy-induced changes in gravid achondroplastic patients further complicate the anesthetic management. The unavailability of proper guidelines and controversies regarding proper anesthetic techniques, drug choice, dosage, and involvement of multiple organ systems challenges anesthesiologists. Here, we present a case of a gravid achondroplastic patient, with a height of 112 cm and mild thoracolumbar scoliosis with intrauterine fetal death in labor, scheduled for emergency lower segment cesarean section and who was managed successfully with spinal anesthesia using low dose anesthetic agents.

Author Biographies

Asha Pun, Pokhara Academy of Health Sciences, Ramghat-10, Pokhara 33700

Anesthesiologist, Department of Anesthesia

Rohini Sigdel, Pokhara Academy of Health Sciences, Ramghat-10, Pokhara 33700

Senior Consultant Anesthesiologist, Department of Anesthesia

References

1. Jain A, Jain K, Makkar JK, Mangal K. Case study: Anaesthetic management of an achondroplastic dwarf undergoing radical nephrectomy. South African J Anaesth Analg. 2010;16(2):77-9. 

https://doi.org/10.1080/22201173.2010.10872668 

2. Shirazi M, Golshahi F, Teimoory N. Successful delivery in a woman with achondroplasia: A case report. Acta Med Iran. 2017;55(8):536-7. [PMiD:29034653] [Full-text]

3. Saxena KN, Kapoor D, Taneja B, Maini L, Hora S. Anaesthetic Management of Caesarean Section in an Achondroplastic Dwarf. Indian J Anaesth. 2008;52(6):844-8. [Full-text]

4. Samra T, Sharma S. Estimation of the dose of hyperbaric bupivacaine for spinal anaesthesia for emergency Caesarean section in an achondroplastic dwarf. Indian J Anaesth. 2010;54:481-2. 

https://doi.org/10.4103/0019-5049.71030 [PMid:21189897] [PMCid:PMC2991669]

5. Li X, Duan H, Zuo M. Case report : anesthesia management for emergency cesarean section in a patient with dwarfism. BMC Anesthesiol [Internet]. 2015;3-5.

https://doi.org/10.1186/s12871-015-0048-2 [PMid:25928113] [PMCid:PMC4429931]

6. Mitra S, Dey N, Gomber KK. Emergency cesarean section in a patient with achondroplasia: An anesthetic diliemma. J Anaesthesiol Clin Pharmacol. 2007;23(3):315-8. [Full-text]

7. Madanmohan, Bayer R, Damor M, Dindor B. Successful Spinal Anesthesia in a Case of Achondroplastic Parturient for Cesarean Section : Case Report. Int J Heal Sci Res. 2016;6(December):360-3. [Full-text]

8. Ravenscroft A, Govender T, Rout C. Spinal anaesthesia for emergency caesarean section in an achondroplastic dwarf. Anaesthesia. 1998;53(12):1236-7. 

https://doi.org/10.1046/j.1365-2044.1998.0716q.x [PMid:10193245]

9. Osorio Rudas W, Socha García NI, Upegui A, Ríos Medina Á, Moran A, Aguirre Ospina O, et al. Anesthesia for cesarean section in a patient with achondroplasia. Colomb J Anesthesiol. 2012;40(4):309-12. 

https://doi.org/10.1016/j.rcae.2012.07.004  

10. Haldar R, Ambesh P, Kaushal A. Anesthesia for an achondroplastic individual with coexisting atlantoaxial dislocation. Anesth Essays Res. 2015;9(3):443. 

https://doi.org/10.4103/0259-1162.158514  [PMid:26712995] [PMCid:PMC4683485]

Downloads

Published

2020-09-08

How to Cite

Pun, A., & Sigdel, R. (2020). A case of achondroplasia for emergency cesarean section. Journal of Society of Anesthesiologists of Nepal, 7(2), e284. Retrieved from http://www.jsan.org.np/jsan/index.php/jsan/article/view/284